EARLY FEEDING AND LIVER DISEASE IN αl-ANTITRYPSIN DEFICIENCY
نویسندگان
چکیده
منابع مشابه
Liver disease and alpha 1-antitrypsin deficiency.
Discovery of AAT deficiency by Laurell and Eriksson in 1963 [2] provided a foundation for current thinking about the pathogenesis of pulmonary emphysema [3,4]. Although AAT deficiency has become one of the best understood genetic disorders at a molecular and protein level, many questions about the clinical disease remain unanswered. Current American and International research projects should pr...
متن کاملAlpha 1-antitrypsin deficiency, complement activation, and chronic liver disease.
Activation of the complement system, the main humoral mediator of inflammation, is restrained by the action of enzyme inhibitors including alpha 1-antitrypsin. Deficiency leads to chronic liver disease in about one in five children with this genetic defect. Complement activation was investigated in 34 children with alpha 1 AT deficiency (12 with minimal, 10 with moderate, and 12 with severe liv...
متن کاملLiver replacement for alpha1-antitrypsin deficiency.
A 16-year-old girl with advanced cirrhosis and severe alpha 1-antitrypsin deficiency of the homozygous Pi ZZ phenotype was treated by orthotopic liver transplantation. After replacement of the liver with a homograft from a donor with the normal Pi MM phenotype, the alpha 1-antitrypsin concentration in the recipient's serum rose to normal; it had the Pi MM phenotype. Two and a third years later,...
متن کاملThe role of Vitamin Deficiency in Early Parkinson's Disease
جهت تعیین ارتباط کمبود ویتامین C با بیماری پارکینسون زودرس، مطالعه ای مشاهده ای از اکتبر ۱۹۸۹ تا جولای ۱۹۹۰ بر روی تمام بیماران کهنسال پذیرفته شده به خانه های مسکونی باری الوکال (محدوده سنی ۹۸-۶۱ سال، سن متوسط 45/ 83، SD + 7/56) توسط مؤلف و سپس با ارجاع به پرستار مشاور در مراکز جامعه انجام شد. در این مطالعه تمام بیماران از نظر علائم بیماری پارکینسون زودرس مورد آزمایش قرار گرفتند و در صورت ...
متن کاملFlecainide and elevated liver enzymes in α1-antitrypsin deficiency
deficiency David J.A. Jenkins, MD, PhD, FRCP, Michael Freeman, MD, FRCPC, Iqwal Mangat, MD, FRCPC, Koruba Srichaikul, MD, MSc, Viranda H. Jayalath, MSc, Dorothea Faulkner, RD, PhD, John L. Sievenpiper, MD, PhD, FRCPC, Cyril W.C. Kendall, PhD, Alexander Romaschin, PhD, Young-In Kim, MD, FRCPC, Paul Dorian, MD, FRCPC, FHRS From the Department of Nutritional Sciences, Faculty of Medicine, Universi...
متن کاملذخیره در منابع من
با ذخیره ی این منبع در منابع من، دسترسی به آن را برای استفاده های بعدی آسان تر کنید
ژورنال
عنوان ژورنال: Pediatric Research
سال: 1984
ISSN: 0031-3998,1530-0447
DOI: 10.1203/00006450-198404001-00736